ICD-10-CM J84.178: Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

ICD-10-CM Diagnosis Code (2025)

Official Description for J84.178

Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Coding Notes & Guidelines for J84.178

Code First
  • underlying disease, such as:
  • progressive systemic sclerosis (M34.0)
  • rheumatoid arthritis (M05.00-M06.9)
  • systemic lupus erythematosis (M32.0-M32.9)
Inclusion Terms
  • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
  • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
  • Organizing pneumonia due to collagen vascular disease
  • Organizing pneumonia in diseases classified elsewhere

Parent Code (Less Specific):

About ICD-10-CM Code J84.178 (Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere)

ICD-10-CM code J84.178 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM J84.178 became effective on October 1, 2024.

This page provides detailed information about J84.178 - Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere.