ICD-10-CM Diagnosis Code (2025)
Official Description for M04
Autoinflammatory syndromes
Coding Notes & Guidelines for M04
Excludes2: Not Included Here
Crohn's disease (K50.-)
Inclusion Terms
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
Inclusion Terms
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
Inclusion Terms
- Blau syndrome
- Deficiency of interleukin 1 receptor antagonist [DIRA]
- Majeed syndrome
- Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
- Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
Child Codes (More Specific Codes for M04):
About ICD-10-CM Code M04 (Autoinflammatory syndromes)
ICD-10-CM code M04 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM M04 became effective on October 1, 2024.
This page provides detailed information about M04 - Autoinflammatory syndromes. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Autoinflammatory syndromes.