ICD-10-CM M04.2: Cryopyrin-associated periodic syndromes

ICD-10-CM Diagnosis Code (2025)

Official Description for M04.2

Cryopyrin-associated periodic syndromes

Coding Notes & Guidelines for M04.2

Inclusion Terms
  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • Familial cold autoinflammatory syndrome
  • Familial cold urticaria
  • Muckle-Wells syndrome
  • Neonatal onset multisystemic inflammatory disorder [NOMID]

Parent Code (Less Specific):

About ICD-10-CM Code M04.2 (Cryopyrin-associated periodic syndromes)

ICD-10-CM code M04.2 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM M04.2 became effective on October 1, 2024.

This page provides detailed information about M04.2 - Cryopyrin-associated periodic syndromes. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Cryopyrin-associated periodic syndromes.