ICD-10-CM M04.8: Other autoinflammatory syndromes

ICD-10-CM Diagnosis Code (2025)

Official Description for M04.8

Other autoinflammatory syndromes

Coding Notes & Guidelines for M04.8

Inclusion Terms
  • Blau syndrome
  • Deficiency of interleukin 1 receptor antagonist [DIRA]
  • Majeed syndrome
  • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
  • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]

Parent Code (Less Specific):

About ICD-10-CM Code M04.8 (Other autoinflammatory syndromes)

ICD-10-CM code M04.8 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM M04.8 became effective on October 1, 2024.

This page provides detailed information about M04.8 - Other autoinflammatory syndromes. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other autoinflammatory syndromes.