ICD-10-CM M35: Other systemic involvement of connective tissue

ICD-10-CM Diagnosis Code (2025)

Official Description for M35

Other systemic involvement of connective tissue

Coding Notes & Guidelines for M35

Excludes1: Not Coded Here

reactive perforating collagenosis (L87.1)

Excludes1: Not Coded Here

dry mouth, unspecified (R68.2)

Excludes1: Not Coded Here

polyangiitis overlap syndrome (M30.8)

Excludes1: Not Coded Here

polymyalgia rheumatica with giant cell arteritis (M31.5)

Excludes1: Not Coded Here
  • lupus panniculitis (L93.2)
  • panniculitis NOS (M79.3-)
Excludes1: Not Coded Here

ligamentous laxity, NOS (M24.2-)

Excludes2: Not Included Here

Ehlers-Danlos syndromes (Q79.6-)

Code First

, if applicable, COVID-19 (U07.1)

Use Additional Code

code to identify associated manifestations

Use Additional Code
  • code, if applicable, for:
  • exposure to COVID-19 or SARS-CoV-2 infection (Z20.822)
  • personal history of COVID-19 (Z86.16)
  • post COVID-19 condition (U09.9)
Inclusion Terms

Sicca syndrome

Inclusion Terms

Renal tubular acidosis in sicca syndrome

Inclusion Terms

Mixed connective tissue disease

Inclusion Terms

Familial ligamentous laxity

Inclusion Terms
  • MIS-A
  • MIS-C
  • Multisystem inflammatory syndrome in adults
  • Multisystem inflammatory syndrome in children
  • Pediatric inflammatory multisystem syndrome
  • PIMS
Inclusion Terms
  • Autoimmune disease (systemic) NOS
  • Collagen (vascular) disease NOS
Code Also
  • any associated complications such as:
  • acute hepatic failure (K72.0-)
  • acute kidney failure (N17.-)
  • acute myocarditis (I40.-)
  • acute respiratory distress syndrome (J80)
  • cardiac arrhythmia (I47-I49.-)
  • pneumonia due to COVID-19 (J12.82)
  • severe sepsis (R65.2-)
  • viral cardiomyopathy (B33.24)
  • viral pericarditis (B33.23)

Child Codes (More Specific Codes for M35):

About ICD-10-CM Code M35 (Other systemic involvement of connective tissue)

ICD-10-CM code M35 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM M35 became effective on October 1, 2024.

This page provides detailed information about M35 - Other systemic involvement of connective tissue. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other systemic involvement of connective tissue.