ICD-10-CM N01: Rapidly progressive nephritic syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for N01

Rapidly progressive nephritic syndrome

Coding Notes & Guidelines for N01

Includes Notes
  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis
Excludes1: Not Coded Here

nephritic syndrome NOS (N05.-)

Excludes1: Not Coded Here
  • Rapidly progressive nephritic syndrome with C3 glomerulonephritis (N01.A)
  • Rapidly progressive nephritic syndrome with C3 glomerulopathy (N01.A)
Excludes1: Not Coded Here

Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6)

Inclusion Terms

Rapidly progressive nephritic syndrome with minimal change lesion

Inclusion Terms
  • Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
  • Rapidly progressive nephritic syndrome with focal and segmental sclerosis
  • Rapidly progressive nephritic syndrome with focal glomerulonephritis
Inclusion Terms

Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS

Inclusion Terms
  • Rapidly progressive nephritic syndrome with C3 glomerulopathy with dense deposit disease
  • Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, type 2
Inclusion Terms

Rapidly progressive nephritic syndrome with extracapillary glomerulonephritis

Inclusion Terms

Rapidly progressive nephritic syndrome with proliferative glomerulonephritis NOS

Inclusion Terms

Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS

Child Codes (More Specific Codes for N01):

N01.0 - Rapidly progressive nephritic syndrome with minor glomerular abnormality N01.1 - Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions N01.2 - Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis N01.3 - Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis N01.4 - Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis N01.5 - Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis N01.6 - Rapidly progressive nephritic syndrome with dense deposit disease N01.7 - Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis N01.8 - Rapidly progressive nephritic syndrome with other morphologic changes N01.9 - Rapidly progressive nephritic syndrome with unspecified morphologic changes N01.A - Rapidly progressive nephritic syndrome with C3 glomerulonephritis

About ICD-10-CM Code N01 (Rapidly progressive nephritic syndrome)

ICD-10-CM code N01 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM N01 became effective on October 1, 2024.

This page provides detailed information about N01 - Rapidly progressive nephritic syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Rapidly progressive nephritic syndrome.