ICD-10-CM N04: Nephrotic syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for N04

Nephrotic syndrome

Coding Notes & Guidelines for N04

Includes Notes
  • congenital nephrotic syndrome
  • lipoid nephrosis
Excludes1: Not Coded Here
  • Nephrotic syndrome with C3 glomerulonephritis (N04.A)
  • Nephrotic syndrome with C3 glomerulopathy (N04.A)
Excludes1: Not Coded Here

Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6)

Code First

, if applicable, other disease or disorder or poisoning causing membranous nephropathy

Use Additional Code

code, if applicable, for adverse effect of drug causing membranous nephropathy

Inclusion Terms

Nephrotic syndrome with minimal change lesion

Inclusion Terms
  • Nephrotic syndrome with focal and segmental hyalinosis
  • Nephrotic syndrome with focal and segmental sclerosis
  • Nephrotic syndrome with focal glomerulonephritis
Inclusion Terms

Membranous nephropathy NOS with nephrotic syndrome

Inclusion Terms

Idiopathic membranous nephropathy with nephrotic syndrome

Inclusion Terms

Nephrotic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS

Inclusion Terms
  • Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
  • Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2
Inclusion Terms

Nephrotic syndrome with extracapillary glomerulonephritis

Inclusion Terms

Nephrotic syndrome with proliferative glomerulonephritis NOS

Inclusion Terms

Nephrotic syndrome with C3 glomerulopathy

Child Codes (More Specific Codes for N04):

N04.0 - Nephrotic syndrome with minor glomerular abnormality N04.1 - Nephrotic syndrome with focal and segmental glomerular lesions N04.2 - Nephrotic syndrome with diffuse membranous glomerulonephritis N04.20 - Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified N04.21 - Primary membranous nephropathy with nephrotic syndrome N04.22 - Secondary membranous nephropathy with nephrotic syndrome N04.29 - Other nephrotic syndrome with diffuse membranous glomerulonephritis N04.3 - Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis N04.4 - Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis N04.5 - Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis N04.6 - Nephrotic syndrome with dense deposit disease N04.7 - Nephrotic syndrome with diffuse crescentic glomerulonephritis N04.8 - Nephrotic syndrome with other morphologic changes N04.9 - Nephrotic syndrome with unspecified morphologic changes N04.A - Nephrotic syndrome with C3 glomerulonephritis

About ICD-10-CM Code N04 (Nephrotic syndrome)

ICD-10-CM code N04 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM N04 became effective on October 1, 2024.

This page provides detailed information about N04 - Nephrotic syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Nephrotic syndrome.