ICD-10-CM Q00: Anencephaly and similar malformations

ICD-10-CM Diagnosis Code (2025)

Official Description for Q00

Anencephaly and similar malformations

Coding Notes & Guidelines for Q00

Inclusion Terms
  • Acephaly
  • Acrania
  • Amyelencephaly
  • Hemianencephaly
  • Hemicephaly

Child Codes (More Specific Codes for Q00):

About ICD-10-CM Code Q00 (Anencephaly and similar malformations)

ICD-10-CM code Q00 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q00 became effective on October 1, 2024.

This page provides detailed information about Q00 - Anencephaly and similar malformations. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Anencephaly and similar malformations.