ICD-10-CM Q04: Other congenital malformations of brain

ICD-10-CM Diagnosis Code (2025)

Official Description for Q04

Other congenital malformations of brain

Coding Notes & Guidelines for Q04

Excludes1: Not Coded Here
  • cyclopia (Q87.0)
  • macrocephaly (Q75.3)
Excludes1: Not Coded Here

congenital malformations of corpus callosum (Q04.0)

Excludes1: Not Coded Here

acquired porencephalic cyst (G93.0)

Inclusion Terms

Agenesis of corpus callosum

Inclusion Terms
  • Absence of part of brain
  • Agenesis of part of brain
  • Agyria
  • Aplasia of part of brain
  • Hydranencephaly
  • Hypoplasia of part of brain
  • Lissencephaly
  • Microgyria
  • Pachygyria
Inclusion Terms
  • Porencephaly
  • Schizencephaly
Inclusion Terms
  • Arnold-Chiari syndrome, type IV
  • Macrogyria
Inclusion Terms
  • Congenital anomaly NOS of brain
  • Congenital deformity NOS of brain
  • Congenital disease or lesion NOS of brain
  • Multiple anomalies NOS of brain, congenital

Child Codes (More Specific Codes for Q04):

Q04.0 - Congenital malformations of corpus callosum Q04.1 - Arhinencephaly Q04.2 - Holoprosencephaly Q04.3 - Other reduction deformities of brain Q04.4 - Septo-optic dysplasia of brain Q04.5 - Megalencephaly Q04.6 - Congenital cerebral cysts Q04.8 - Other specified congenital malformations of brain Q04.9 - Congenital malformation of brain, unspecified

About ICD-10-CM Code Q04 (Other congenital malformations of brain)

ICD-10-CM code Q04 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q04 became effective on October 1, 2024.

This page provides detailed information about Q04 - Other congenital malformations of brain. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other congenital malformations of brain.