ICD-10-CM Q23: Congenital malformations of aortic and mitral valves

ICD-10-CM Diagnosis Code (2025)

Official Description for Q23

Congenital malformations of aortic and mitral valves

Coding Notes & Guidelines for Q23

Excludes1: Not Coded Here
  • congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
  • congenital subaortic stenosis (Q24.4)
  • supravalvular aortic stenosis (congenital) (Q25.3)
Inclusion Terms
  • Congenital aortic atresia
  • Congenital aortic stenosis NOS
Inclusion Terms

Congenital aortic insufficiency

Inclusion Terms

Congenital mitral atresia

Inclusion Terms
  • Congenital bicuspid aortic valve
  • Unicuspid (congenital) aortic valve (at birth)
Inclusion Terms

Cleft mitral valve leaflet at birth

Code Also
  • , if applicable, acquired aortic valve disorders, such as:
  • aortic (valve) insufficiency (nonrheumatic) (I35.1)
  • aortic (valve) stenosis (nonrheumatic) (I35.0)
  • aortic (valve) stenosis with insufficiency (nonrheumatic) (I35.2)

Child Codes (More Specific Codes for Q23):

About ICD-10-CM Code Q23 (Congenital malformations of aortic and mitral valves)

ICD-10-CM code Q23 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q23 became effective on October 1, 2024.

This page provides detailed information about Q23 - Congenital malformations of aortic and mitral valves. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformations of aortic and mitral valves.