ICD-10-CM Q25: Congenital malformations of great arteries

ICD-10-CM Diagnosis Code (2025)

Official Description for Q25

Congenital malformations of great arteries

Coding Notes & Guidelines for Q25

Excludes1: Not Coded Here
  • congenital aortic stenosis NOS (Q23.0)
  • congenital stenosis of aortic valve (Q23.0)
Excludes1: Not Coded Here

hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)

Inclusion Terms
  • Patent ductus Botallo
  • Persistent ductus arteriosus
Inclusion Terms
  • Coarctation of aorta (preductal) (postductal)
  • Stenosis of aorta
Inclusion Terms

Atresia of aortic arch

Inclusion Terms

Atresia of aorta

Inclusion Terms
  • Congenital aneurysm of aortic root
  • Congenital aneurysm of aortic sinus
Inclusion Terms

Vascular ring of aorta

Inclusion Terms

Persistent convolutions of aortic arch

Inclusion Terms

Persistent right aortic arch

Inclusion Terms
  • Aortic arch
  • Bovine arch
Inclusion Terms

Supravalvular pulmonary stenosis

Inclusion Terms

Congenital pulmonary arteriovenous aneurysm

Inclusion Terms
  • Aberrant pulmonary artery
  • Agenesis of pulmonary artery
  • Congenital aneurysm of pulmonary artery
  • Congenital anomaly of pulmonary artery
  • Hypoplasia of pulmonary artery

Child Codes (More Specific Codes for Q25):

About ICD-10-CM Code Q25 (Congenital malformations of great arteries)

ICD-10-CM code Q25 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q25 became effective on October 1, 2024.

This page provides detailed information about Q25 - Congenital malformations of great arteries. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformations of great arteries.