ICD-10-CM Q26: Congenital malformations of great veins

ICD-10-CM Diagnosis Code (2025)

Official Description for Q26

Congenital malformations of great veins

Coding Notes & Guidelines for Q26

Inclusion Terms

Congenital stenosis of vena cava (inferior)(superior)

Inclusion Terms
  • Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
  • Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
Inclusion Terms

Partial anomalous pulmonary venous return

Inclusion Terms
  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome
Inclusion Terms

Congenital anomaly of vena cava (inferior) (superior) NOS

Child Codes (More Specific Codes for Q26):

Q26.0 - Congenital stenosis of vena cava Q26.1 - Persistent left superior vena cava Q26.2 - Total anomalous pulmonary venous connection Q26.3 - Partial anomalous pulmonary venous connection Q26.4 - Anomalous pulmonary venous connection, unspecified Q26.5 - Anomalous portal venous connection Q26.6 - Portal vein-hepatic artery fistula Q26.8 - Other congenital malformations of great veins Q26.9 - Congenital malformation of great vein, unspecified

About ICD-10-CM Code Q26 (Congenital malformations of great veins)

ICD-10-CM code Q26 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q26 became effective on October 1, 2024.

This page provides detailed information about Q26 - Congenital malformations of great veins. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformations of great veins.