ICD-10-CM Q33: Congenital malformations of lung

ICD-10-CM Diagnosis Code (2025)

Official Description for Q33

Congenital malformations of lung

Coding Notes & Guidelines for Q33

Excludes1: Not Coded Here
  • cystic fibrosis (E84.0)
  • cystic lung disease, acquired or unspecified (J98.4)
Excludes1: Not Coded Here

pulmonary hypoplasia associated with short gestation (P28.0)

Inclusion Terms
  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease
Inclusion Terms

Azygos lobe (fissured), lung

Inclusion Terms

Congenital absence of lung (lobe)

Child Codes (More Specific Codes for Q33):

Q33.0 - Congenital cystic lung Q33.1 - Accessory lobe of lung Q33.2 - Sequestration of lung Q33.3 - Agenesis of lung Q33.4 - Congenital bronchiectasis Q33.5 - Ectopic tissue in lung Q33.6 - Congenital hypoplasia and dysplasia of lung Q33.8 - Other congenital malformations of lung Q33.9 - Congenital malformation of lung, unspecified

About ICD-10-CM Code Q33 (Congenital malformations of lung)

ICD-10-CM code Q33 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q33 became effective on October 1, 2024.

This page provides detailed information about Q33 - Congenital malformations of lung. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformations of lung.