ICD-10-CM Q40.0: Congenital hypertrophic pyloric stenosis

ICD-10-CM Diagnosis Code (2025)

Official Description for Q40.0

Congenital hypertrophic pyloric stenosis

Coding Notes & Guidelines for Q40.0

Inclusion Terms
  • Congenital or infantile constriction
  • Congenital or infantile hypertrophy
  • Congenital or infantile spasm
  • Congenital or infantile stenosis
  • Congenital or infantile stricture

Parent Code (Less Specific):

About ICD-10-CM Code Q40.0 (Congenital hypertrophic pyloric stenosis)

ICD-10-CM code Q40.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q40.0 became effective on October 1, 2024.

This page provides detailed information about Q40.0 - Congenital hypertrophic pyloric stenosis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital hypertrophic pyloric stenosis.