ICD-10-CM Q44: Congenital malformations of gallbladder, bile ducts and liver

ICD-10-CM Diagnosis Code (2025)

Official Description for Q44

Congenital malformations of gallbladder, bile ducts and liver

Coding Notes & Guidelines for Q44

Inclusion Terms

Congenital absence of gallbladder

Inclusion Terms
  • Congenital malformation of gallbladder NOS
  • Intrahepatic gallbladder
Inclusion Terms
  • Accessory hepatic duct
  • Biliary duct duplication
  • Congenital malformation of bile duct NOS
  • Cystic duct duplication
Inclusion Terms

Fibrocystic disease of liver

Inclusion Terms

Congenital malformation of liver, NOS

Inclusion Terms

Alagille-Watson syndrome

Inclusion Terms
  • Accessory liver
  • Congenital absence of liver
  • Congenital hepatomegaly
Code Also

, if applicable, associated malformations affecting other systems

Child Codes (More Specific Codes for Q44):

Q44.0 - Agenesis, aplasia and hypoplasia of gallbladder Q44.1 - Other congenital malformations of gallbladder Q44.2 - Atresia of bile ducts Q44.3 - Congenital stenosis and stricture of bile ducts Q44.4 - Choledochal cyst Q44.5 - Other congenital malformations of bile ducts Q44.6 - Cystic disease of liver Q44.7 - Other congenital malformations of liver Q44.70 - Other congenital malformation of liver, unspecified Q44.71 - Alagille syndrome Q44.79 - Other congenital malformations of liver

About ICD-10-CM Code Q44 (Congenital malformations of gallbladder)

ICD-10-CM code Q44 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q44 became effective on October 1, 2024.

This page provides detailed information about Q44 - Congenital malformations of gallbladder, bile ducts and liver. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformations of gallbladder related to bile ducts and liver.