ICD-10-CM Q56: Indeterminate sex and pseudohermaphroditism

ICD-10-CM Diagnosis Code (2025)

Official Description for Q56

Indeterminate sex and pseudohermaphroditism

Coding Notes & Guidelines for Q56

Excludes1: Not Coded Here
  • 46,XX true hermaphrodite (Q99.1)
  • androgen insensitivity syndrome (E34.5-)
  • chimera 46,XX/46,XY true hermaphrodite (Q99.0)
  • female pseudohermaphroditism with adrenocortical disorder (E25.-)
  • pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
  • pure gonadal dysgenesis (Q99.1)
Inclusion Terms

Ovotestis

Inclusion Terms
  • 46, XY with streak gonads
  • Male pseudohermaphroditism NOS
Inclusion Terms

Female pseudohermaphroditism NOS

Inclusion Terms

Ambiguous genitalia

Child Codes (More Specific Codes for Q56):

Q56.0 - Hermaphroditism, not elsewhere classified Q56.1 - Male pseudohermaphroditism, not elsewhere classified Q56.2 - Female pseudohermaphroditism, not elsewhere classified Q56.3 - Pseudohermaphroditism, unspecified Q56.4 - Indeterminate sex, unspecified

About ICD-10-CM Code Q56 (Indeterminate sex and pseudohermaphroditism)

ICD-10-CM code Q56 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q56 became effective on October 1, 2024.

This page provides detailed information about Q56 - Indeterminate sex and pseudohermaphroditism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Indeterminate sex and pseudohermaphroditism.