ICD-10-CM Q61: Cystic kidney disease

ICD-10-CM Diagnosis Code (2025)

Official Description for Q61

Cystic kidney disease

Coding Notes & Guidelines for Q61

Excludes1: Not Coded Here
  • acquired cyst of kidney (N28.1)
  • Potter's syndrome (Q60.6)
Excludes1: Not Coded Here

polycystic kidney disease (Q61.11-Q61.3)

Inclusion Terms

Cyst of kidney NOS (congenital)

Inclusion Terms

Polycystic kidney, autosomal recessive

Inclusion Terms

Polycystic kidney, autosomal dominant

Inclusion Terms
  • Multicystic dysplastic kidney
  • Multicystic kidney (development)
  • Multicystic kidney disease
  • Multicystic renal dysplasia
Inclusion Terms
  • Nephronophthisis
  • Sponge kidney NOS
Inclusion Terms
  • Fibrocystic kidney
  • Fibrocystic renal degeneration or disease
Inclusion Terms

Meckel-Gruber syndrome

Child Codes (More Specific Codes for Q61):

About ICD-10-CM Code Q61 (Cystic kidney disease)

ICD-10-CM code Q61 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q61 became effective on October 1, 2024.

This page provides detailed information about Q61 - Cystic kidney disease. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Cystic kidney disease.