ICD-10-CM Q82: Other congenital malformations of skin

ICD-10-CM Diagnosis Code (2025)

Official Description for Q82

Other congenital malformations of skin

Coding Notes & Guidelines for Q82

Excludes1: Not Coded Here
  • acrodermatitis enteropathica (E83.2)
  • congenital erythropoietic porphyria (E80.0)
  • pilonidal cyst or sinus (L05.-)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89)
Excludes1: Not Coded Here
  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
Excludes1: Not Coded Here

Ellis-van Creveld syndrome (Q77.6)

Excludes1: Not Coded Here

Ehlers-Danlos syndromes (Q79.6-)

Excludes2: Not Included Here
  • Café au lait spots (L81.3)
  • lentigo (L81.4)
  • nevus NOS (D22.-)
  • araneus nevus (I78.1)
  • melanocytic nevus (D22.-)
  • pigmented nevus (D22.-)
  • spider nevus (I78.1)
  • stellar nevus (I78.1)
Excludes2: Not Included Here
  • pilonidal cyst with abscess (L05.01)
  • pilonidal cyst without abscess (L05.91)
Inclusion Terms
  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa
Inclusion Terms
  • Birthmark NOS
  • Flammeus Nevus
  • Portwine Nevus
  • Sanguineous Nevus
  • Strawberry Nevus
  • Vascular Nevus NOS
  • Verrucous Nevus
Inclusion Terms

Parasacral dimple

Inclusion Terms
  • Abnormal palmar creases
  • Accessory skin tags
  • Benign familial pemphigus [Hailey-Hailey]
  • Congenital poikiloderma
  • Cutis laxa (hyperelastica)
  • Dermatoglyphic anomalies
  • Inherited keratosis palmaris et plantaris
  • Keratosis follicularis [Darier-White]

Child Codes (More Specific Codes for Q82):

Q82.0 - Hereditary lymphedema Q82.1 - Xeroderma pigmentosum Q82.2 - Congenital cutaneous mastocytosis Q82.3 - Incontinentia pigmenti Q82.4 - Ectodermal dysplasia (anhidrotic) Q82.5 - Congenital non-neoplastic nevus Q82.6 - Congenital sacral dimple Q82.8 - Other specified congenital malformations of skin Q82.9 - Congenital malformation of skin, unspecified

About ICD-10-CM Code Q82 (Other congenital malformations of skin)

ICD-10-CM code Q82 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q82 became effective on October 1, 2024.

This page provides detailed information about Q82 - Other congenital malformations of skin. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other congenital malformations of skin.