ICD-10-CM Q87.1: Congenital malformation syndromes predominantly associated with short stature

ICD-10-CM Diagnosis Code (2025)

Official Description for Q87.1

Congenital malformation syndromes predominantly associated with short stature

Coding Notes & Guidelines for Q87.1

Excludes1: Not Coded Here
  • Ellis-van Creveld syndrome (Q77.6)
  • Smith-Lemli-Opitz syndrome (E78.72)
Inclusion Terms
  • Aarskog syndrome
  • Cockayne syndrome
  • De Lange syndrome
  • Dubowitz syndrome
  • Noonan syndrome
  • Robinow-Silverman-Smith syndrome
  • Russell-Silver syndrome
  • Seckel syndrome

Parent Code (Less Specific):

About ICD-10-CM Code Q87.1 (Congenital malformation syndromes predominantly associated with short stature)

ICD-10-CM code Q87.1 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q87.1 became effective on October 1, 2024.

This page provides detailed information about Q87.1 - Congenital malformation syndromes predominantly associated with short stature. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital malformation syndromes predominantly associated with short stature.