ICD-10-CM Q87.8: Other specified congenital malformation syndromes, not elsewhere classified

ICD-10-CM Diagnosis Code (2025)

Official Description for Q87.8

Other specified congenital malformation syndromes, not elsewhere classified

Coding Notes & Guidelines for Q87.8

Excludes1: Not Coded Here

Zellweger syndrome (E71.510)

Use Additional Code

code to identify stage of chronic kidney disease (N18.1-N18.6)

Inclusion Terms
  • Asadollahi-Rauch syndrome
  • Mediator complex subunit 13L syndrome
Code Also
  • , if applicable, any associated manifestations such as:
  • autism spectrum disorder (F84.0-)
  • congenital malformations of cardiac septa (Q21.-)
  • epilepsy and recurrent seizures (G40.-)
  • intellectual disability (F70-F79)

Parent Code (Less Specific):

About ICD-10-CM Code Q87.8 (Other specified congenital malformation syndromes)

ICD-10-CM code Q87.8 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q87.8 became effective on October 1, 2024.

This page provides detailed information about Q87.8 - Other specified congenital malformation syndromes, not elsewhere classified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other specified congenital malformation syndromes related to not elsewhere classified.