ICD-10-CM Q89: Other congenital malformations, not elsewhere classified

ICD-10-CM Diagnosis Code (2025)

Official Description for Q89

Other congenital malformations, not elsewhere classified

Coding Notes & Guidelines for Q89

Excludes1: Not Coded Here

isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)

Excludes1: Not Coded Here
  • adrenogenital disorders (E25.-)
  • congenital adrenal hyperplasia (E25.0)
Excludes1: Not Coded Here
  • congenital goiter (E03.0)
  • congenital hypothyroidism (E03.1)
Excludes1: Not Coded Here

dextrocardia NOS (Q24.0)

Excludes1: Not Coded Here

congenital malformation syndromes affecting multiple systems (Q87.-)

Use Additional Code

code(s) to identify all associated manifestations

Inclusion Terms

Congenital splenomegaly

Inclusion Terms
  • Congenital malformation of parathyroid or thyroid gland
  • Persistent thyroglossal duct
  • Thyroglossal cyst
Inclusion Terms
  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera
Inclusion Terms
  • Craniopagus
  • Dicephaly
  • Pygopagus
  • Thoracopagus
Inclusion Terms
  • Multiple congenital anomalies NOS
  • Multiple congenital deformities NOS
Inclusion Terms
  • Congenital anomaly NOS
  • Congenital deformity NOS

Child Codes (More Specific Codes for Q89):

Q89.0 - Congenital absence and malformations of spleen Q89.01 - Asplenia (congenital) Q89.09 - Congenital malformations of spleen Q89.1 - Congenital malformations of adrenal gland Q89.2 - Congenital malformations of other endocrine glands Q89.3 - Situs inversus Q89.4 - Conjoined twins Q89.7 - Multiple congenital malformations, not elsewhere classified Q89.8 - Other specified congenital malformations Q89.9 - Congenital malformation, unspecified

About ICD-10-CM Code Q89 (Other congenital malformations)

ICD-10-CM code Q89 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM Q89 became effective on October 1, 2024.

This page provides detailed information about Q89 - Other congenital malformations, not elsewhere classified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other congenital malformations related to not elsewhere classified.